Abstract
Zinners syndrome refers to rare malformations and is characterized by a triad of signs - unilateral renal agenesis, obstruction of the vas deferens, and cystic transformation of the seminal vesicle. A description of a clinical case of Zinners syndrome with an atypical clinical picture is presented. This observation indicates the need for an in-depth examination of the genital organs in men with renal agenesis.