Restriction of Calpain3 Expression to the Skeletal Muscle Prevents Cardiac Toxicity and Corrects Pathology in a Murine Model of Limb-Girdle Muscular Dystrophy-Reference-Cited by-同舟云学术

Restriction of Calpain3 Expression to the Skeletal Muscle Prevents Cardiac Toxicity and Corrects Pathology in a Murine Model of Limb-Girdle Muscular Dystrophy

Published:2013-09-03 Issue:10 Volume:128 Page:1094-1104
ISSN:0009-7322
Container-title:Circulation
language:en
Short-container-title:Circulation

Author:

Roudaut Carinne¹,Le Roy Florence¹,Suel Laurence¹,Poupiot Jérôme¹,Charton Karine¹,Bartoli Marc¹,Richard Isabelle¹

Affiliation:

1. From Généthon, CNRS-UMR8587, Evry, France (C.R., F.LR., L.S., J.P., K.C., M.B., I.R.); and Université d’Evry Val d’Essonne, Evry, France (F.L.R.).

Publisher

Ovid Technologies (Wolters Kluwer Health)

Subject

Physiology (medical),Cardiology and Cardiovascular Medicine

Reference25 articles.

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2. Molecular cloning of a novel mammalian calcium-dependent protease distinct from both m- and mu-types. Specific expression of the mRNA in skeletal muscle.;Sorimachi H;J Biol Chem,1989

3. Calpain 3 Is Activated through Autolysis within the Active Site and Lyses Sarcomeric and Sarcolemmal Components

4. Ca2+ Dependency of Calpain 3 (p94) Activation

5. Null mutation of calpain 3 (p94) in mice causes abnormal sarcomere formation in vivo and in vitro

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