Multicenter study of combination DEP regimen as a salvage therapy for adult refractory hemophagocytic lymphohistiocytosis

Author:

Wang Yini1,Huang Wenqiu1,Hu Liangding2,Cen Xinan3,Li Lihong4,Wang Jijun5,Shen Jianliang6,Wei Na1,Wang Zhao1

Affiliation:

1. Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, China;

2. Department of Transplatation, Affiliated Hospital Academy of Military Medical Sciences, Beijing, China;

3. Department of Hematology, Peking University First Hospital, Beijing, China;

4. Department of Hematology, Beijing Chao-yang Hospital, Capital Medical University, Beijing, China;

5. Department of Hematology, Peking University Third Hospital, Beijing, China; and

6. Department of Hematology, Navy General Hospital, Beijing, China

Abstract

Key Points A salvage therapy for adults with refractory hemophagocytic lymphohistiocytosis. Liposomal doxorubicin treatment combined with etoposide and methylprednisolone showed an encouraging overall response and was well-tolerated.

Publisher

American Society of Hematology

Subject

Cell Biology,Hematology,Immunology,Biochemistry

Reference26 articles.

1. Familial hemophagocytic lymphohistiocytosis.;Janka;Eur J Pediatr,1983

2. Treatment of hemophagocytic lymphohistiocytosis with HLH-94 immunochemotherapy and bone marrow transplantation.;Henter;Blood,2002

3. Unrelated donor hematopoietic cell transplantation for hemophagocytic lymphohistiocytosis.;Baker;Bone Marrow Transplant,2008

4. Adult haemophagocytic syndrome.;Ramos-Casals;Lancet,2014

5. [Clinical characteristics of 192 adult hemophagocytic lymphohistiocytosis].;Huang;Zhonghua Xue Ye Xue Za Zhi,2014

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