Role of βArg211 in the Active Site of Human β-Hexosaminidase B-Reference-Cited by-同舟云学术

Role of βArg211 in the Active Site of Human β-Hexosaminidase B

Published:2000-05-01 Issue:20 Volume:39 Page:6219-6227
ISSN:0006-2960
Container-title:Biochemistry
language:en
Short-container-title:Biochemistry

Author:

Hou Yongmin¹,Vocadlo David¹,Withers Stephen¹,Mahuran Don¹

Affiliation:

1. The Research Institute, The Hospital for Sick Children, Toronto, Ontario M5G 1X8, Canada, Department of Laboratory Medicine and Pathobiology, Toronto, Ontario M5G 2C4, Canada, and Department of Chemistry, University of British Columbia, Vancouver, British Columbia V6T 1Z1, Canada

Publisher

American Chemical Society (ACS)

Subject

Biochemistry

Link

https://pubs.acs.org/doi/pdf/10.1021/bi992464j

Reference49 articles.

1. Assignment of β-hexosaminidase A α-subunit to human chromosomal region 15q23→q24

2. Xmnl RFLP at 5q13 detected by a 0.49 kb Xmn I fragment of human hexosaminidase (HEXB) cDNA

3. Isolation of cDNA clones coding for the alpha-subunit of human beta-hexosaminidase. Extensive homology between the alpha- and beta-subunits and studies on Tay-Sachs disease.

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