Affiliation:
1. National Medical Research Center for Hematology
Abstract
Introduction. Primary immune thrombocytopenia (ITP) is an autoimmune disease caused by the production of antibodies to the membrane structures of platelets and their precursors — megakaryocytes, which causes not only increased destruction of platelets, but also inadequate thrombocytopoiesis, characterized by isolated thrombocytopenia below 100.0×109/L and the presence/absence of hemorrhagic syndrome of varying severity.Aim: to present modern recommendations for the diagnosis and treatment of ITPBasic information. The recommendations are based on the experience of Russian and international experts, the leadership of the international working group on the study of primary immune thrombocytopenia, and recommendations of the European and American Societies of Hematology using new data on the development and course of ITP. Approaches to the treatment of the disease using new drugs from the group of thrombopoietin receptor agonists are present
Publisher
National Medical Research Center of Hematology of the Ministry of Health of the Russian Federation
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