Prognostic factors of early death in a cohort of 162 adult haemophagocytic syndrome: impact of triggering disease and early treatment with etoposide

Author:

Arca Marc1,Fardet Laurence23,Galicier Lionel4,Rivière Sébastien235,Marzac Christophe6,Aumont Cédric7,Lambotte Olivier89,Coppo Paul2101112

Affiliation:

1. Service d'Hématologie Pédiatrique; Caen France

2. Faculté de Médecine Pierre et Marie Curie; Univ Paris 06; UPMC Sorbonne Université; Paris France

3. Service de Médecine Interne; AP-HP, Hôpital Saint Antoine; Paris France

4. Départment d'Immunologie Clinique; AP-HP, Hôpital Saint-Louis; Univ Paris Diderot; Sorbonne Paris Cité; Paris France

5. Departement Hospitalo-Universitaire; UPMC; Paris France

6. Service d'Hématologie Biologique; AP-HP, Hôpital Saint Antoine; Paris France

7. Service d'Hématologie Biologique; AP-HP, Hôpital de Bicêtre; Paris France

8. Service de Médecine Interne - Immunologie Clinique; AP-HP, Hôpital de Bicêtre; Le Kremlin Bicêtre France

9. Université Paris-Sud 11; Le Kremlin Bicêtre France

10. Service d'Hématologie; AP-HP, Hôpital Saint Antoine; Paris France

11. Centre de Référence des Microangiopathies Thrombotiques; Paris France

12. Institut Gustave Roussy; INSERM U1009; Villejuif France

Publisher

Wiley

Subject

Hematology

Reference28 articles.

1. Treatment factors affecting outcomes in HIV-associated non-Hodgkin lymphomas: a pooled analysis of 1546 patients;Barta;Blood,2013

2. Hemophagocytic syndrome in HIV infection;Bourquelot;Presse Medicale (Paris, France: 1983),1993

3. Critical care management of patients with hemophagocytic lymphohistiocytosis;Buyse;Intensive Care Medicine,2010

4. Hematophagic histiocytosis: a clinicopathologic analysis of 23 cases with special reference to the association with peripheral T-cell lymphoma;Chang;Journal of the Formosan Medical Association,1994

5. A proportion of patients with lymphoma may harbor mutations of the perforin gene;Clementi;Blood,2005

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