Rescue by elexacaftor-tezacaftor-ivacaftor of the G1244E cystic fibrosis mutation's stability and gating defects are dependent on cell background
Author:
Publisher
Elsevier BV
Subject
Pulmonary and Respiratory Medicine,Pediatrics, Perinatology and Child Health
Reference45 articles.
1. Cystic fibrosis genetics: from molecular understanding to clinical application;Cutting;Nat Rev Genet,2015
2. CFTR Modulators: the Changing Face of Cystic Fibrosis in the Era of Precision Medicine;Lopes-Pacheco;Front Pharmacol,2019
3. Cystic fibrosis: a clinical view;Castellani;Cell Mol Life Sci,2017
4. Structure, Gating, and Regulation of the Cftr Anion Channel;Csanady;Physiol Rev,2019
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