Modern Approaches to the Management of Children with Atypical Hemolytic Uremic Syndrome-Reference-Cited by-同舟云学术

Modern Approaches to the Management of Children with Atypical Hemolytic Uremic Syndrome

Published:2022-04-21 Issue:2 Volume:19 Page:127-152
ISSN:2500-3089
Container-title:Pediatric pharmacology
language:
Short-container-title:Pediatr. farmakol.

Author:

Emirova Khadizha M.¹^ORCID,Abaseeva Tatiana Yu.¹^ORCID,Baranov Alexander A.²^ORCID,Vashakmadze Nato D.³^ORCID,Vishneva Elena A.³^ORCID,Generalova Galina A.⁴^ORCID,Zakharova Ekaterina Yu.⁵^ORCID,Kaluzhnaya Tatiana A.³^ORCID,Kutsev Sergey I.⁵^ORCID,Namazova-Baranova Leyla S.⁶^ORCID,Makarova Tamara P.⁷^ORCID,Margieva Tea V.⁸^ORCID,Mstislavskaya Sofya A.¹,Muzurov Aleksandr L.⁴^ORCID,Pankratenko Tatiana E.⁹^ORCID,Shilova Marina M.¹⁰^ORCID,Fedoseenko Marina V.³^ORCID

Affiliation:

1. A.I. Yevdokimov Moscow State University of Medicine and Dentistry; Center of Gravitational Blood Surgery and Hemodialysis of Saint Vladimir Children’s Clinical Hospital

2. Research Institute of Pediatrics and Children's Health in Petrovsky National Research Centre of Surgery; Sechenov First Moscow State Medical University

3. Research Institute of Pediatrics and Children's Health in Petrovsky National Research Centre of Surgery; Pirogov Russian National Research Medical University

4. Center of Gravitational Blood Surgery and Hemodialysis of Saint Vladimir Children’s Clinical Hospital; Russian Medical Academy of Continuing Professional Education

5. Research Centre for Medical Genetics

6. Research Institute of Pediatrics and Children's Health in Petrovsky National Research Centre of Surgery; Pirogov Russian National Research Medical University; Belgorod National Research University

7. Kazan State Medical University

8. Sechenov First Moscow State Medical University

9. Center of Gravitational Blood Surgery and Hemodialysis of Saint Vladimir Children’s Clinical Hospital

10. Pirogov Russian National Research Medical University

Abstract

Experts of the Union of Pediatricians of Russia have developed modern guidelines on management of children with atypical hemolytic uremic syndrome (aHUS). aHUS is ultra-rare (orphan) disease with progressive and relapsing course during the life with potentially life-threatening state. This article covers issues of disease etiology, pathogenesis, and classification. Specific attention is paid to the diagnosis, differential diagnosis, and therapy of aHUS according to the evidence-based approaches.

Publisher

Paediatrician Publishers LLC

Subject

Pulmonary and Respiratory Medicine,Pediatrics, Perinatology and Child Health

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