Increased Urinary Excretion of 3-Oxo-Δ4 Bile Acids in Japanese Patients with Idiopathic Neonatal Cholestasis-Reference-Cited by-同舟云学术

Increased Urinary Excretion of 3-Oxo-Δ4 Bile Acids in Japanese Patients with Idiopathic Neonatal Cholestasis

Published:1998-11 Issue:5 Volume:27 Page:606-609
ISSN:0277-2116
Container-title:Journal of Pediatric Gastroenterology & Nutrition
language:en
Short-container-title:Journal of Pediatric Gastroenterology & Nutrition

Author:

Kimura Akihiko,Suzuki Mikako,Tohma Masahiko,Inoue Toshiro,Endo Fumio,Kagimoto Seiichi,Matsui Akira,Kawai Masahiko,Hayashi Motohiko,Iizuka Toshiyuki,Tajiri Hitoshi,Kato Hirohisa

Publisher

Ovid Technologies (Wolters Kluwer Health)

Subject

Gastroenterology,Pediatrics, Perinatology and Child Health

Reference11 articles.

1. 3-OXO-Δ4 BILE ACIDS IN LIVER DISEASE

2. Inborn errors of bile acid metabolism

3. Delta 4-3-oxosteroid 5 beta-reductase deficiency described in identical twins with neonatal hepatitis. A new inborn error in bile acid synthesis.

4. Δ4-3-Oxosteroid 5β-reductase deficiency causing neonatal liver failure and hemochromatosis

5. Delta 4-3-oxosteroid 5 beta-reductase deficiency: failure of ursodeoxycholic acid treatment and response to chenodeoxycholic acid plus cholic acid.

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1. The role of 5-reduction in physiology and metabolic disease: evidence from cellular, pre-clinical and human studies;The Journal of Steroid Biochemistry and Molecular Biology;2021-03

2. SRD5B1gene analysis needed for the accurate diagnosis of primary 3-oxo-Δ4-steroid 5β-reductase deficiency;Journal of Gastroenterology and Hepatology;2009-05

3. Mutations in SRD5B1 (AKR1D1), the gene encoding 4-3-oxosteroid 5 -reductase, in hepatitis and liver failure in infancy;Gut;2003-10-01

4. Mass Spectrometry in the Clinical Laboratory;Chemical Reviews;2001-01-09