Hb S/β-Thalassemia in the REDS-III Brazil Sickle Cell Disease Cohort: Clinical, Laboratory and Molecular Characteristics

Author:

Belisário André R.1ORCID,Carneiro-Proietti Anna B.1ORCID,Sabino Ester Cerdeira2ORCID,Araújo Aderson3,Loureiro Paula34ORCID,Máximo Cláudia5ORCID,Flor-Park Miriam V.6ORCID,Rodrigues Daniela D.O.W.1ORCID,Ozahata Mina Cintho7ORCID,McClure Christopher8,Mota Rosimere Afonso1ORCID,Gomes Moura Isabel C.9ORCID,Custer Brian1011ORCID,Kelly Shannon1012ORCID,

Affiliation:

1. Fundação Hemominas, Minas Gerais, Brazil;

2. Faculdade de Medicina (FMUSP), Instituto de Medicina Tropical, Universidade de São Paulo, São Paulo, Brazil;

3. Fundação Hemope, Pernambuco, Brazil;

4. Universidade de Pernambuco, Pernambuco, Brazil;

5. Hemorio, Rio de Janeiro, Brazil;

6. Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo, Instituto da Criança, São Paulo, Brazil;

7. Departamento de Ciências da Computação, Universidade de São Paulo, São Paulo, Brazil;

8. Research Triangle Institute (RTI), Rockville, MD, USA;

9. Faculdade Ciências Médicas de Minas Gerais, Brazil;

10. Vitalant Research Institute, San Francisco, CA, USA;

11. Department of Laboratory Medicine, University of California San Francisco (UCSF), San Francisco, CA, USA;

12. UCSF, Benioff Children’s Hospital Oakland, Oakland, CA, USA

Publisher

Informa UK Limited

Subject

Biochemistry (medical),Clinical Biochemistry,Genetics (clinical),Hematology

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